Thymic carcinoid associated with multiple endocrine neoplasia syndrome type I.

نویسندگان

  • José Luis Recuero Díaz
  • Raúl Embún Flor
  • Patricia Menal Muñoz
  • Jorge Hernández Ferrández
  • Miguel Jesús Arrarás Martínez
  • Juan José Rivas de Andrés
چکیده

Thymic carcinoids are a rare entity that may be associated with endocrine diseases like Cushing's syndrome or multiple endocrine neoplasia syndrome type I (MEN1). These tumors represent 4% of anterior mediastinal tumors and are characterized by their very aggressive behavior. We present the case of a patient with a previous MEN 1 diagnosis in whom, during the follow up of his disease, a thoracic image compatible with thymic carcinoid was detected. After an extended thymectomy that included peri-thymic fat resection, the clinical diagnosis was confirmed. A follow up examination 14 months later revealed a suspicious lesion that suggested local recurrence, therefore the patient was reoperated on. The pathology report of this surgery indicated post-radiation fibrosis. Likewise, we present a review of the current diagnostic and therapeutic management of patients with MEN1 syndrome who are diagnosed with thymic carcinoid.

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عنوان ژورنال:
  • Archivos de bronconeumologia

دوره 49 3  شماره 

صفحات  -

تاریخ انتشار 2013